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2-Hydroxy-2-methylbutanoic acid (Standard) [3739-30-8]

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2-Hydroxy-2-methylbutanoic acid (Standard) [3739-30-8] : Size : 1L - Certification : Research Use Only - 2-Hydroxy-2-methylbutanoic acid (Standard) is the analytical standard of 2-Hydroxy-2-methylbutanoic acid. This product is intended for research and analytical applications. 2-Hydroxy-2-methylbutanoic acid, an unusual metabolite, is associated with 2-hydroxyglutaric aciduria and maple syrup urine disease. -

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